Persistent Pneumomediastinum and Dermatomyositis
361
1
2. Jansen TL ThA, Barrera P, Van Engelen BGM et al.
Dermatomyositis with subclinical myositis and spontaneous
pneumomediastinum with pneumothorax: Case report and
review of the literature. Clin Exp Rheumatol 1998;16:733–5.
3. Isfer RS, Nakao SK, Cernea SS. Dermatomyositis associated with
pneumomediastinum and subcutaneous cellular tissue emphyse-
ma (letter). Br J Rheumatol 1994;33:1092.
4. Kobayashi N, Takizawa H, Sugiyama H. A case of dermoto-
myositis which rapidly developed to respiratory failure in the
presence of pneumomediastinum. Nihon-Kyobu-Shikkan-Gakkai-
Zasshi 1989;27:848–54.
without any complication. He was on long-term steroid
therapy, including repeated high-dose methylpredniso-
lone IV pulse therapy. He suffered from interstitial lung
disease, which improved on steroids, and had no
associated pneumothorax.
1
1
Conclusion
We report the case of a 42-year-old man with
dermatomyositis, who subsequently developed pneumo-
mediastinum which persists 12 months after diagnosis.
Various mechanisms have been proposed to explain this
association. However, it should be stressed that
pneumomediastinum is not an uncommon complication
of dermatomyositis and that its aetiopathogenesis
remains very unclear.
1
1
1
5. Gayraud M, Lhote F, Valeyre D et al. Pneumothorax et
pneumom e´ diastin associ e´ s a` une dermatomyosite. Ann Med
Interne 1989;140:490–1.
6. Santiago MB, Chalhoub M, Taden Pereira S. Amyopathic
dermatomyositis complicated by interstitial pulmonary disease
and pneumomediastinum (letter). J Rheumatol 1998;25:2042–3.
7. Satomi K, Michibata T, Iizuka H, Hukuda H, Miyashita T.
Recurrent pneumomediastinum in the course of interstitial
pneumonia associated with dermatomyositis. Nihon-Kokyuki-
Gakkai-Zasshi 1998;36:984–8.
1
1
2
2
8. Bousquet E, Rolland Y, Bon E. Pneumomediastinum, a rare
complication of dermatomyositis. Report of a case. Rev Rhum
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1
Received for publication 26 July 2000
Accepted in revised form 14 March 2001